16 relations: Alpha-Ketoglutaric acid, Aminolevulinic acid, Aminolevulinic acid synthase, Citric acid cycle, Coenzyme A, Decarboxylation, Glycine, Hydrolysis, Methylmalonyl-CoA, Methylmalonyl-CoA mutase, Oxoglutarate dehydrogenase complex, Porphyrin, Propionyl-CoA, Succinic acid, Succinyl coenzyme A synthetase, Vitamin B12.
α-Ketoglutaric acid (2-oxoglutaric acid) is one of two ketone derivatives of glutaric acid.
δ-Aminolevulinic acid (also dALA, δ-ALA, 5ALA or 5-aminolevulinic acid), an endogenous non-protein amino acid, is the first compound in the porphyrin synthesis pathway, the pathway that leads to heme in mammals and chlorophyll in plants.
Aminolevulinic acid synthase (ALA synthase, ALAS, or delta-aminolevulinic acid synthase) is an enzyme that catalyzes the synthesis of D-aminolevulinic acid (ALA) the first common precursor in the biosynthesis of all tetrapyrroles such as hemes, cobalamins and chlorophylls.
The citric acid cycle (CAC) – also known as the tricarboxylic acid (TCA) cycle or the Krebs cycle – is a series of chemical reactions used by all aerobic organisms to release stored energy through the oxidation of acetyl-CoA derived from carbohydrates, fats, and proteins into carbon dioxide and chemical energy in the form of adenosine triphosphate (ATP).
Coenzyme A (CoA,SCoA,CoASH) is a coenzyme, notable for its role in the synthesis and oxidation of fatty acids, and the oxidation of pyruvate in the citric acid cycle.
Decarboxylation is a chemical reaction that removes a carboxyl group and releases carbon dioxide (CO2).
Glycine (symbol Gly or G) is the amino acid that has a single hydrogen atom as its side chain.
Hydrolysis is a term used for both an electro-chemical process and a biological one.
Methylmalonyl-CoA is the thioester consisting of coenzyme A linked to methylmalonic acid.
Methylmalonyl-CoA mutase (MCM), mitochondrial, also known as methylmalonyl-CoA isomerase, is a protein that in humans is encoded by the MUT gene.
The oxoglutarate dehydrogenase complex (OGDC) or α-ketoglutarate dehydrogenase complex is an enzyme complex, most commonly known for its role in the citric acid cycle.
Porphyrins (/phɔɹfɚɪn/ ''POUR-fer-in'') are a group of heterocyclic macrocycle organic compounds, composed of four modified pyrrole subunits interconnected at their α carbon atoms via methine bridges (.
Propionyl-CoA is a coenzyme A derivative of propionic acid.
Succinic acid is a dicarboxylic acid with the chemical formula (CH2)2(CO2H)2.
Succinyl coenzyme A synthetase (SCS, also known as succinyl-CoA synthetase or succinate thiokinase or succinate-CoA ligase) is an enzyme that catalyzes the reversible reaction of succinyl-CoA to succinate.
Vitamin B12, also called cobalamin, is a water-soluble vitamin that is involved in the metabolism of every cell of the human body: it is a cofactor in DNA synthesis, and in both fatty acid and amino acid metabolism.