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ICD-10 Chapter IV: Endocrine, nutritional and metabolic diseases and Sphingolipidoses

Shortcuts: Differences, Similarities, Jaccard Similarity Coefficient, References.

Difference between ICD-10 Chapter IV: Endocrine, nutritional and metabolic diseases and Sphingolipidoses

ICD-10 Chapter IV: Endocrine, nutritional and metabolic diseases vs. Sphingolipidoses

This is an overview about the chapter IV (also called chapter E) of the International Statistical Classification of Diseases and Related Health Problems 10th Revision (ICD-10). Sphingolipidoses (singular "sphingolipidosis") are a class of lipid storage disorders relating to sphingolipid metabolism.

Similarities between ICD-10 Chapter IV: Endocrine, nutritional and metabolic diseases and Sphingolipidoses

ICD-10 Chapter IV: Endocrine, nutritional and metabolic diseases and Sphingolipidoses have 10 things in common (in Unionpedia): Fabry disease, Gangliosidosis, Gaucher's disease, GM1 gangliosidoses, Intellectual disability, Lipid storage disorder, Niemann–Pick disease, Sandhoff disease, Sphingolipid, Tay–Sachs disease.

Fabry disease

Fabry disease is a rare genetic disease.

Fabry disease and ICD-10 Chapter IV: Endocrine, nutritional and metabolic diseases · Fabry disease and Sphingolipidoses · See more »

Gangliosidosis

Gangliosidosis contains different types of lipid storage disorders caused by the accumulation of lipids known as gangliosides.

Gangliosidosis and ICD-10 Chapter IV: Endocrine, nutritional and metabolic diseases · Gangliosidosis and Sphingolipidoses · See more »

Gaucher's disease

Gaucher's disease or Gaucher disease (GD) is a genetic disorder in which glucocerebroside (a sphingolipid, also known as glucosylceramide) accumulates in cells and certain organs.

Gaucher's disease and ICD-10 Chapter IV: Endocrine, nutritional and metabolic diseases · Gaucher's disease and Sphingolipidoses · See more »

GM1 gangliosidoses

The GM1 gangliosidoses (or GM1 gangliosidosis) are caused by a deficiency of beta-galactosidase, with resulting abnormal storage of acidic lipid materials in cells of the central and peripheral nervous systems, but particularly in the nerve cells.

GM1 gangliosidoses and ICD-10 Chapter IV: Endocrine, nutritional and metabolic diseases · GM1 gangliosidoses and Sphingolipidoses · See more »

Intellectual disability

Intellectual disability (ID), also known as general learning disability, and mental retardation (MR), is a generalized neurodevelopmental disorder characterized by significantly impaired intellectual and adaptive functioning.

ICD-10 Chapter IV: Endocrine, nutritional and metabolic diseases and Intellectual disability · Intellectual disability and Sphingolipidoses · See more »

Lipid storage disorder

A lipid storage disorder (or lipidosis) can be any one of a group of inherited metabolic disorders in which harmful amounts of fats or lipids accumulate in some of the body’s cells and tissues.

ICD-10 Chapter IV: Endocrine, nutritional and metabolic diseases and Lipid storage disorder · Lipid storage disorder and Sphingolipidoses · See more »

Niemann–Pick disease

Niemann–Pick disease is a group of inherited, severe metabolic disorders in which sphingomyelin accumulates in lysosomes in cells.

ICD-10 Chapter IV: Endocrine, nutritional and metabolic diseases and Niemann–Pick disease · Niemann–Pick disease and Sphingolipidoses · See more »

Sandhoff disease

Sandhoff disease, also known as Sandhoff–Jatzkewitz disease, variant 0 of GM2-Gangliosidosis or Hexosaminidase A and B deficiency, is a lysosomal genetic, lipid storage disorder caused by the inherited deficiency to create functional beta-hexosaminidases A and B. These catabolic enzymes are needed to degrade the neuronal membrane components, ganglioside GM2, its derivative GA2, the glycolipid globoside in visceral tissues, and some oligosaccharides.

ICD-10 Chapter IV: Endocrine, nutritional and metabolic diseases and Sandhoff disease · Sandhoff disease and Sphingolipidoses · See more »

Sphingolipid

Sphingolipids are a class of lipids containing a backbone of sphingoid bases, a set of aliphatic amino alcohols that includes sphingosine.

ICD-10 Chapter IV: Endocrine, nutritional and metabolic diseases and Sphingolipid · Sphingolipid and Sphingolipidoses · See more »

Tay–Sachs disease

Tay–Sachs disease is a genetic disorder that results in the destruction of nerve cells in the brain and spinal cord.

ICD-10 Chapter IV: Endocrine, nutritional and metabolic diseases and Tay–Sachs disease · Sphingolipidoses and Tay–Sachs disease · See more »

The list above answers the following questions

ICD-10 Chapter IV: Endocrine, nutritional and metabolic diseases and Sphingolipidoses Comparison

ICD-10 Chapter IV: Endocrine, nutritional and metabolic diseases has 388 relations, while Sphingolipidoses has 48. As they have in common 10, the Jaccard index is 2.29% = 10 / (388 + 48).

References

This article shows the relationship between ICD-10 Chapter IV: Endocrine, nutritional and metabolic diseases and Sphingolipidoses. To access each article from which the information was extracted, please visit:

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