Similarities between ICD-10 Chapter IV: Endocrine, nutritional and metabolic diseases and Sphingolipidoses
ICD-10 Chapter IV: Endocrine, nutritional and metabolic diseases and Sphingolipidoses have 10 things in common (in Unionpedia): Fabry disease, Gangliosidosis, Gaucher's disease, GM1 gangliosidoses, Intellectual disability, Lipid storage disorder, Niemann–Pick disease, Sandhoff disease, Sphingolipid, Tay–Sachs disease.
Fabry disease
Fabry disease is a rare genetic disease.
Fabry disease and ICD-10 Chapter IV: Endocrine, nutritional and metabolic diseases · Fabry disease and Sphingolipidoses ·
Gangliosidosis
Gangliosidosis contains different types of lipid storage disorders caused by the accumulation of lipids known as gangliosides.
Gangliosidosis and ICD-10 Chapter IV: Endocrine, nutritional and metabolic diseases · Gangliosidosis and Sphingolipidoses ·
Gaucher's disease
Gaucher's disease or Gaucher disease (GD) is a genetic disorder in which glucocerebroside (a sphingolipid, also known as glucosylceramide) accumulates in cells and certain organs.
Gaucher's disease and ICD-10 Chapter IV: Endocrine, nutritional and metabolic diseases · Gaucher's disease and Sphingolipidoses ·
GM1 gangliosidoses
The GM1 gangliosidoses (or GM1 gangliosidosis) are caused by a deficiency of beta-galactosidase, with resulting abnormal storage of acidic lipid materials in cells of the central and peripheral nervous systems, but particularly in the nerve cells.
GM1 gangliosidoses and ICD-10 Chapter IV: Endocrine, nutritional and metabolic diseases · GM1 gangliosidoses and Sphingolipidoses ·
Intellectual disability
Intellectual disability (ID), also known as general learning disability, and mental retardation (MR), is a generalized neurodevelopmental disorder characterized by significantly impaired intellectual and adaptive functioning.
ICD-10 Chapter IV: Endocrine, nutritional and metabolic diseases and Intellectual disability · Intellectual disability and Sphingolipidoses ·
Lipid storage disorder
A lipid storage disorder (or lipidosis) can be any one of a group of inherited metabolic disorders in which harmful amounts of fats or lipids accumulate in some of the body’s cells and tissues.
ICD-10 Chapter IV: Endocrine, nutritional and metabolic diseases and Lipid storage disorder · Lipid storage disorder and Sphingolipidoses ·
Niemann–Pick disease
Niemann–Pick disease is a group of inherited, severe metabolic disorders in which sphingomyelin accumulates in lysosomes in cells.
ICD-10 Chapter IV: Endocrine, nutritional and metabolic diseases and Niemann–Pick disease · Niemann–Pick disease and Sphingolipidoses ·
Sandhoff disease
Sandhoff disease, also known as Sandhoff–Jatzkewitz disease, variant 0 of GM2-Gangliosidosis or Hexosaminidase A and B deficiency, is a lysosomal genetic, lipid storage disorder caused by the inherited deficiency to create functional beta-hexosaminidases A and B. These catabolic enzymes are needed to degrade the neuronal membrane components, ganglioside GM2, its derivative GA2, the glycolipid globoside in visceral tissues, and some oligosaccharides.
ICD-10 Chapter IV: Endocrine, nutritional and metabolic diseases and Sandhoff disease · Sandhoff disease and Sphingolipidoses ·
Sphingolipid
Sphingolipids are a class of lipids containing a backbone of sphingoid bases, a set of aliphatic amino alcohols that includes sphingosine.
ICD-10 Chapter IV: Endocrine, nutritional and metabolic diseases and Sphingolipid · Sphingolipid and Sphingolipidoses ·
Tay–Sachs disease
Tay–Sachs disease is a genetic disorder that results in the destruction of nerve cells in the brain and spinal cord.
ICD-10 Chapter IV: Endocrine, nutritional and metabolic diseases and Tay–Sachs disease · Sphingolipidoses and Tay–Sachs disease ·
The list above answers the following questions
- What ICD-10 Chapter IV: Endocrine, nutritional and metabolic diseases and Sphingolipidoses have in common
- What are the similarities between ICD-10 Chapter IV: Endocrine, nutritional and metabolic diseases and Sphingolipidoses
ICD-10 Chapter IV: Endocrine, nutritional and metabolic diseases and Sphingolipidoses Comparison
ICD-10 Chapter IV: Endocrine, nutritional and metabolic diseases has 388 relations, while Sphingolipidoses has 48. As they have in common 10, the Jaccard index is 2.29% = 10 / (388 + 48).
References
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