13 relations: Cystathionine beta synthase, Cystathionine gamma-lyase, Cystathioninuria, Cysteine, Cysteine dioxygenase, Glutamate–cysteine ligase, Glutathione, Glutathione synthetase, Homocysteine, Hypotaurine, Serine, Taurine, Transsulfuration pathway.
Cystathionine beta synthase
Cystathionine-β-synthase, also known as CBS, is an enzyme that in humans is encoded by the CBS gene.
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Cystathionine gamma-lyase
Cystathionine gamma-lyase (CTH or CSE; also cystathionase) is an enzyme which breaks down cystathionine into cysteine, α-ketobutyrate, and ammonia.
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Cystathioninuria
Cystathioninuria, also called cystathionase deficiency, is an autosomal recessive metabolic disorder that results in an excess of cystathionine in the urine.
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Cysteine
Cysteine (symbol Cys or C) is a semi-essential proteinogenic amino acid with the formula HO2CCH(NH2)CH2SH.
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Cysteine dioxygenase
Cysteine dioxygenase (CDO, CAS number: 37256-59-0) is a mammalian non-heme iron enzyme that catalyzes the conversion of L-cysteine to cysteine sulfinic acid (cysteine sulfinate) via the incorporation of two dioxygen-derived oxygens.
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Glutamate–cysteine ligase
Glutamate Cysteine Ligase (GCL), previously known as gamma-glutamylcysteine synthetase (GCS), is the first enzyme of the cellular glutathione (GSH) biosynthetic pathway that catalyzes the chemical reaction: L-glutamate + L-cysteine + ATP \rightleftharpoons gamma-glutamyl cysteine + ADP + Pi GSH, and by extension GCL, is critical to cell survival.
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Glutathione
Glutathione (GSH) is an important antioxidant in plants, animals, fungi, and some bacteria and archaea.
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Glutathione synthetase
Glutathione synthetase (GSS) (EC 6.3.2.3) is the second enzyme in the glutathione (GSH) biosynthesis pathway.
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Homocysteine
Homocysteine is a non-proteinogenic α-amino acid.
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Hypotaurine
Hypotaurine is a sulfinic acid that is an intermediate in the biosynthesis of taurine.
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Serine
Serine (symbol Ser or S) is an ɑ-amino acid that is used in the biosynthesis of proteins.
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Taurine
No description.
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Transsulfuration pathway
The transsulfuration pathway is a metabolic pathway involving the interconversion of cysteine and homocysteine, through the intermediate cystathionine.
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